![]() 3, 5– 7 Gamstorp reported an 8 year old girl with GBS by with unconsciousness, oscillating eye movement, and convulsions, and proposed the term “encephalomyeloradiculoneuropathy”. ![]() Although the CNS is rarely involved, GBS associated with CNS manifestations has been described in children, 1, 2, 4 as well as adults. GBS is regarded as a predominantly motor neuropathy with few sensory features. CSF showed 40×10 9/l lymphocytes, no erythrocytes, and 3.56 g/l protein. We firstly suspected acute disseminated encephalomyelitis, but a nerve conduction study on the next day showed remarkable reduction of motor conduction velocity. Magnetic resonance angiography was normal. Cerebral magnetic resonance imaging (MRI) revealed lesions in both frontal and right occipital lobes, which showed low intensity on T1 weighted image and high intensity on T2 weighted image (fig 1). Deep tendon reflexes were absent in all extremities. On admission, she was alert with notable generalised weakness. Cerebral CT on the next day revealed low density areas in the right occipital area. She complained of headache accompanied with meningism on the fourth day of immunoglobulin administration. She was treated with intravenous immunoglobulin (400 mg/kg for five days), but did not improve. Motor and sensory nerve conduction velocity remained normal. Head computed tomography (CT) was normal cerebrospinal fluid (CSF) showed cell count of 1×10 9/l and 89 mg/dl protein. On admission, she was alert but could not stand up. A previously healthy 9 year old girl was admitted to Kamo Hospital because of progressive ascending weakness, beginning five days before admission. ![]()
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